Polycystic kidney disease is an inherited disease characterized by autosomal dominant and recessive genetic disorders. Autosomal dominant polycystic kidney disease is the most common in polycystic kidney disease. The following is tongshantang nephropathy experts give us an introduction of autosomal recessive polycystic kidney.
Autosomal recessive polycystic kidney disease has autosomal recessive inheritance. Almost all parents do not have the same medical history. Autosomal recessive polycystic kidney disease, also called infantile polycystic kidney disease, is suitable for rare polycystic kidney disease. Often die shortly after birth, only a few patients with mild illness can survive to childhood or even adulthood.
Autosomal recessive polycystic kidney disease is pided into prenatal, maternal, infant and infant types. Tongshantang nephropathy experts explain autosomal recessive polycystic kidney:
Autosomal recessive polycystic kidney: prenatal
When there is severe perinatal renal cystic disease involving 90% collecting ducts, while there is a small amount of fibrosis around the portal vein, perinatal death is involved.
Autosomal recessive polycystic kidney: maternal type
Involving 60% collecting ducts accompanied by mild portal fibrosis. Usually die a few months later and die of renal failure.
Autosomal recessive polycystic kidney kidney: infants and young children
The baby type showed bilateral renal enlargement, with 25% kidney, liver, splenomegaly, accompanied by mild portal fibrous hyperplasia. Symptoms occur from 3 to 6 months after birth and die from renal failure.
Autosomal recessive polycystic kidney kidney: juvenile type
Juvenile means age between 13 and 19 years. Renal injury is relatively mild, renal tubules show less than 10% cystic degeneration, and occasionally renal failure. Severe fibrosis of hepatic portal vein. General 20 or so age, due to liver complications, death from portal hypertension.
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